also known as Osteopetrosis, Marble bone disease
osteopetrosis belong to group of disorders causing increased skeletal density due to defect in bone resorption by osteoclasts leading to hyperostosis.
most severe form of disease occurs in utero. progression seen after birth is with anaemia,hepatosplenomegaly hydrocephalus,cranial nerve involvement and death often due to infections.
plain x ray findings includes
1.osteosclerosis